Proteus syndrome: A case report

Authors

  • Baghdadi Taghi
  • Balighi Kamran
  • Espandar Ramin
  • Tork Ali Naser
  • Yazdanian Shideh
Abstract:

The Proteus syndrome comprises an association of asymmetrical overgrowth of almost any part of the body, verrucous epidermal naevi, vascular malformations and lipoma-like subcutaneous hamartoma. Both sexes are affected with equal frequency and severity and it is not transmitted genetically. Here a 16-year-old man with asymmetric overgrowth of the extremities, macrodactyly, cerebriform hypertrophy of the soles and various skin and bony lesions is reported diagnosed as Proteus syndrome.

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Journal title

volume 9  issue 4

pages  360- 366

publication date 2006-12-01

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